Surgical Treatment for Multiple Odontogenic Keratocyst : A Case Report
Keywords:
Odontogenic Keratocyst, Nevoid basal cell carcinoma syndromeAbstract
A 21-year-old female was referred to the Dental Department, Uthaithani Hospital, with multiple cystic lesions in the maxilla and mandible observed on a panoramic radiograph. The patient visited an orthodontist complaining of the failure of permanent teeth to erupt. Extraoral examination revealed multiple palmar pits. Intraoral examination showed a partly edentulous state; teeth 18, 26, 28, 37, 38, 46, and 48 were missing. A panoramic radiograph revealed multiple large radiolucencies with well-defined margins in the posterior maxilla and mandible. A skull radiograph revealed calcification of the falx cerebri. Marsupialization and biopsy of cystic lesions in the right and left mandible were performed under local anesthesia. The histopathologic report confirmed the diagnosis of odontogenic keratocyst (OKC). Based on all clinical, radiographic, and histopathologic findings, this case suggested the possibility of nevoid basal cell carcinoma syndrome (NBCCS). After 10 months of marsupialization, the patient was admitted to the hospital, and enucleation of all cystic lesions was performed under general anesthesia. There were no postoperative complications and no signs of recurrence after a 2-year follow-up.
Keywords: Odontogenic Keratocyst, Nevoid basal cell carcinoma syndrome
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